Hypoplastic Left Heart Syndrome

Hypoplastic Left Heart Syndrome (HLHS) is a condition where the left side chambers of the heart develop too small to work effectively. This is a problem because the left side of the heart pumps blood to the body. With this side being too small, the body does not get the blood it needs. As a result, the baby can become very sick shortly after birth. If this condition is untreated, the baby usually will die.

We have a number of approaches at Children’s Hospital. One option was developed here, and it spares the baby open heart surgery until the baby is older and bigger. This procedure involves stenting of the patent ductus arteriosus (PDA) and banding the blood vessels to the lungs (pulmonary arteries). The baby returns at 4 to 6 months of age for the open heart surgery. Another option is called the “Norwood.” Here the surgeon connects the main blood vessels off the heart to permit blood to be pumped into the body. A tube is then connected from the blood vessel of the body (aorta) to the lung’s blood vessel (pulmonary artery). The baby needs to return at 4 to 6 months of age for another surgery. Both of the above options require the baby to undergo further procedures and surgeries. The third possibility is heart transplantation.

Phelicity's Story

Ben and Veronica Sneesby moved halfway around the world - from Australia to Columbus, Ohio, - for treatment for their daughter's Hypoplastic Left Heart Syndrome. Read their story.

Parent Resource Guide

Want to learn more about Hypoplastic Left Heart Syndrome? Our parent resource guide has information on treatment options and more.